Sturge-Weber syndrome features a port-wine stain with vascular involvement of which structure?

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Multiple Choice

Sturge-Weber syndrome features a port-wine stain with vascular involvement of which structure?

Explanation:
The key concept is that Sturge-Weber involves vascular malformations of the leptomeninges over the brain. In this syndrome, capillary-venous angiomas develop in the pia and arachnoid coverings of the cortex, which leads to cortical changes and seizures. The port-wine stain on the skin is cutaneous, but the neurologic problems arise from these meningeal vascular lesions. Muscles, bone, and nerves aren’t the primary sites of this angiomatosis, so the meninges are the structure most involved.

The key concept is that Sturge-Weber involves vascular malformations of the leptomeninges over the brain. In this syndrome, capillary-venous angiomas develop in the pia and arachnoid coverings of the cortex, which leads to cortical changes and seizures. The port-wine stain on the skin is cutaneous, but the neurologic problems arise from these meningeal vascular lesions. Muscles, bone, and nerves aren’t the primary sites of this angiomatosis, so the meninges are the structure most involved.

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